Prosthetic Rehabilitation in a Child with Hereditary Ectodermal Dysplasia

  • Carlos Henrique R Nunes Professor of the Pos-graduation in Implant Dentistry – Fluminense Federal University. Address: Mario Santos Braga Street, 28 - Centro - Niterói – RJ - Brazil - 24020-140
  • Mariana Campello Nunes Doctorate in Dentistry - School of Dentistry - Fluminense Federal University. Address: Mario Santos Braga Street, 28 - Centro - Niterói – RJ - Brazil - 24020-140
  • Aristides da Rosa Pinheiro Chair of the Pos-graduation in Implant Dentistry – Fluminense Federal University. Address: Mario Santos Braga Street, 28 - Centro - Niterói – RJ - Brazil - 24020-140
  • Cleonicio Cordeiro Filho Professor of the Pos-graduation in Implant Dentistry – Fluminense Federal University. Address: Mario Santos Braga Street, 28 - Centro - Niterói – RJ - Brazil - 24020-140
  • Bruno Cunha Rangel Professor of the Pos-graduation in Implant Dentistry – Fluminense Federal University. Address: Mario Santos Braga Street, 28 - Centro - Niterói – RJ - Brazil - 24020-140
  • Ricardo Villas-Bôas Doctorate in Dentistry - School of Dentistry - Fluminense Federal University. Address: Mario Santos Braga Street, 28 - Centro - Niterói – RJ - Brazil - 24020-140
  • Carlos Fernando de Almeida Barros Mourão Post-graduation program in Dentistry – Fluminense Federal University. Address: Mario Santos Braga Street, 28 - Centro - Niterói – RJ - Brazil - 24020-140
  • Priscila Ladeira Casado Professor of the Pos-graduation in Implant Dentistry – Fluminense Federal University. Address: Mario Santos Braga Street, 28 - Centro - Niterói – RJ - Brazil - 24020-140
Keywords: complete denture, hereditary ectodermal dysplasia, hypodontia, hypotrichosis, hypohidrosis.

Abstract

Hereditary ectodermal dysplasia is a disease linked to the X recessive chromosome that affects the development of tissues derived from the ectoderm. The main clinical manifestations include hypohidrosis (inability to sweat), hypotrichosis (sparse hair) and hypodontia (lack teeth). This work presents a clinical case of a 6-year old male child who had been diagnosed with hereditary ectodermal dysplasia. The treatment consisted of the fabrication of a mandibular and maxillary complete denture to improve his esthetic, functional and psychological conditions.

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Published
2019-03-21
How to Cite
1.
R Nunes C, Nunes M, Pinheiro A, Filho C, Rangel B, Villas-Bôas R, Mourão CF, Casado P. Prosthetic Rehabilitation in a Child with Hereditary Ectodermal Dysplasia. IABCR [Internet]. 21Mar.2019 [cited 21Aug.2019];5(1):57-0. Available from: https://iabcr.org/index.php/iabcr/article/view/465