Steven Johnson Syndrome – A Triad of Mucosal Lesions, Cutaneous Involvement and History of Recent Drug Exposure

  • Hamid Iqbal Assistant Professor & Incharge Intensive Care Unit, Kuwait Teaching Hospital Peshawar.
  • Muhammad Salman Haider Qureshi House Officer, Intensive Care Unit, Kuwait Teaching Hospital Peshawar.
  • Owais Shah Medical Officer, Intensive Care Unit, Kuwait Teaching Hospital Peshawar.
  • Syed Shahmeer Raza Medical Student, Khyber Medical University Peshawar.
Keywords: Steven Johnson Syndrome, Toxic Epidermal Necrolysis

Abstract

Steven Johnson Syndrome is relative a rare but yet an acute life-threatening condition. A middle aged lady presented to us in an emergency condition with high grade fever (104oF), oral mucosal ulcers, purulent discharge from both eyes, photophobia, generalized skin rashes, flank bruises, dyspnea, severe odynophagia along with dysphagia and blisters on both hands and feet. Because of extensive oral thrush, mouth ulcers and purulent discharge from eyes, the patient was initially suspected to be a case of oral candidiasis and bacterial conjunctivitis. However, due to wide spread muco-cutaneous involvement and after obtaining detailed drug history and getting opinion from dermatology and ophthalmology department, a diagnosis of Steven Johnson Syndrome was established. The treatment was started accordingly and the patient responded dramatically to the treatment, got improved and was subsequently discharged.

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References

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Published
2016-06-18
How to Cite
1.
Iqbal H, Qureshi MSH, Shah O, Raza SS. Steven Johnson Syndrome – A Triad of Mucosal Lesions, Cutaneous Involvement and History of Recent Drug Exposure. Int Arch BioMed Clin Res [Internet]. 2016Jun.18 [cited 2019Oct.17];2(2):87-0. Available from: https://iabcr.org/index.php/iabcr/article/view/219